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Idiopathic Ketotic Hypoglycemia is the most common non-iatrogenic cause of hypoglycemia in children beyond infancy. It improves with age and is rare after puberty. Early morning hypoglycemia, responding promptly to glucose, is a typical presentation. Etiology of hypoglycemia is unclear; deficiency of gluconeogenic substrate (hypoalaninemia) has been widely proposed. Idiopathic Ketotic Hypoglyce...

BACKGROUND According to the textbooks, the ketotic glycogen storage disease (GSD) types 0, III, VI, IX, and XI are associated with fasting ketotic hypoglycemia and considered milder as gluconeogenesis is intact. METHODS A retrospective cohort study of biochemical profiles from supervised clinical fasting studies is performed in ketotic GSD patients in our metabolic center. For data analysis, ...

Acute hypoglycemia in children is not an uncommon disease that can be encountered in the Emergency Department. Most cases of childhood hypoglycemia are caused by ketotic hypoglycemia due to missed meals. Often, hypoketotic hypoglycemia can also occur, which suggests hyperinsulinemia or a defect in fatty acid oxidation. Carnitine is essential for long chain fatty acids transfer into mitochondria...

The acute metabolic complications of diabetes consist of diabetic ketoacidosis (DKA), hyperosmolar non-ketotic coma (HNC), lactic acidosis (LA), and hypoglycemia. DKA and HNC are related to insulin deficiency. Hypoglycemia results from the treatment of diabetes, either with oral agents or insulin. Although hypoglycemia may occur in conjunction with oral hypoglycemic therapy, it is more common i...

Type 2 Diabetes Mellitus is one of metabolic disorder, which is characterized by elevation of blood glucose level as consequences of insulin resistance and insulin deficiency. By the history of illness, Diabetic patients because of various condition will experience various complications, either as acute (hypoglycemia, ketoacidosis, and Non-ketotic hyperosmolarity) or chronic complication (macro...

The work of Ulstrom and his associates,"2 has described many of the features of ketotic hypoglycemia, a syndrome of sporadic hypoglycemia associated with ketosis in children. These investigators have described the following characteristics: hypoglycemia rarely occurred before 18 months of age; it usually occurred after poor dietary intake; acetonuria was present; this kind of hypoglycemia was s...